Metastatic Angiosarcoma and Kasabach-Merritt Syndrome
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چکیده
منابع مشابه
Metastatic Angiosarcoma and Kasabach-Merritt Syndrome
Angiosarcomas are exceedingly rare tumors that are often difficult to diagnose. Exceptionally unusual is the presentation of these tumors with Kasabach-Merritt Syndrome, a curious form of intratumoral coagulation that can be impossible to distinguish from intravascular coagulation, which is more common. Instant recognition of this clinical association can help making a prompt diagnosis and time...
متن کاملCutaneous angiosarcoma associated with the Kasabach-Merritt syndrome.
Dear Editor, Angiosarcoma is a rare tumour commonly affecting elderly men, usually occurring on the head and neck region.1 The tumour usually presents as ecchymosis-like plaques, and less commonly with haemorrhage, oedema, ulceration and recurrent facial angioedema. Kasabach-Merritt syndrome (KMS) may occur in association with a vascular tumour and is characterised by consumption of platelets a...
متن کاملKasabach-Merritt syndrome.
Hemangiomas of infancy are usually congenital lesions. Occasionally they are associated with microangiopatbic bemolytic anaemia, thrombocytopenia, and a consumptive coagulopathy. This is most often associated with cavernous hemangiomas. Thrombocytopenia associated with giant cavernous hemangiomas was first noted by Kasabach and Merritt in 1940. As the primary mechanism of platelet destruction i...
متن کاملAbout the Treatment of Kasabach-Merritt Syndrome
94 To the Editor, Dr. Emre and colleagues briefly reported on a 24-year-old female with Kasabach-Merritt syndrome in the most recent issue of this journal [1]. Three units of fresh frozen plasma were administrated within 3 days to the patient for the correction of severe hypofibrinogenemia despite a very high D-dimer level (5000 ng/mL), both of which reflected consumption coagulopathy, as state...
متن کاملHepatic angiosarcoma with clinical and histological features of Kasabach-Merritt syndrome
Hepatic angiosarcoma is a mesenchymal tumor originating from liver sinusoidal endothelial cells. It is an extremely rare malignant neoplasm accounting for less than 1% of primary malignant liver tumors. The deregulated coagulopathy that can be seen in hepatic angiosarcoma fulfills the clinical diagnostic criteria of disseminated intravascular coagulation. However, the mechanism that governs thi...
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ژورنال
عنوان ژورنال: Rare Tumors
سال: 2014
ISSN: 2036-3613,2036-3613
DOI: 10.4081/rt.2014.5366